A 32-year-old female presented with distorted and blurred vision in her right eye. 160° UWF full-range SS-OCTA (montage of two 24mm x 20mm) revealed vascular dilation, tortuosity, and temporal vascular anastomoses (fig. A arrowheads) with extensive nonperfusion (fig. A asterisks) in both eyes. Incontinentia pigmenti was diagnosed based on abnormalities of retinal features, skin and teeth, and family history. Foveal retinoschisis due to vitreomacular traction by the posterior vitreous cortex was detected (fig. B arrows) by high-resolution 24mm B-scan in her right eye.

A 400 kHz speed full-range swept-source OCTA (BMizar, TowardPi Medical) was used in this case to detect peripheral anomalies. An ultra-widefield of view above 200° can be achieved with a flexible montage of 24mm x 20mm full-range OCTA on the device.

This case was published in the Ophthalmology, authored by Dr. Yongwei Guo and Dr. Fang Zhang, the team of Prof. Li Zhang from the Second Affiliated Hospital, School of Medicine, Zhejiang University.

Link to the original text: https://www.ophthalmologyretina.org/article/S2468-6530(24)00005-8/fulltext